| 中文名称: | 盐酸美格鲁特 | ||||
|---|---|---|---|---|---|
| 英文名称: | Miglustat hydrochloride | ||||
| 别名: | 盐酸美格鲁特 N-Butyldeoxynojirimycin hydrochloride; NB-DNJ hydrochloride; OGT 918 hydrochloride | ||||
| CAS No: | 210110-90-0 | 分子式: | C10H21NO4 | 分子量: | 219.28 |
| CAS No: | 210110-90-0 | ||||
| 分子式: | C10H21NO4 | ||||
| 分子量: | 219.28 | ||||
一种葡萄糖神经酰胺合成酶抑制剂，可作用于 I 型戈谢病。
Miglustat, also known as OGT 918 and NB-DNJ, is a drug developed by Actelion and is used primarily to treat Type I Gaucher disease (GD1). Miglustat inhibits glucosylceramide synthase, an essential enzyme for the synthesis of most glycosphingolipids (it forms glucosylceramide and accumulates within the macrophages). Miglustat is used to treat adults with mild-to-moderate Type I Gaucher disease and it is the first treatment to be approved for patients with Niemann–Pick type C disease.
本计算器可帮助您计算出特定溶液中溶质的质量、溶液浓度和体积之间的关系，公式为：
质量 (g) = 浓度 (mol/L) x 体积 (L) x 分子量 (g/mol)
摩尔浓度计算公式
用本工具协助配置特定浓度的溶液，使用的计算公式为：
开始浓度 x 开始体积 = 最终浓度 x 最终体积
稀释公式
稀释公式一般简略地表示为：C1V1 = C2V2 ( 输入 输出 )
